Paniz Pourpashang
1 
, Seyed Mohammad Taghi Hosseini Tabatabaei
1 , Minoo Fallahi
2 , Leily Mohajerzadeh
3 , Arefeh Zahmatkesh
4* 1 Department of Pediatric Nephrology, Shahid Beheshti University of Medical Sciences, Tehran, Iran
2 Neonatal Health Research Center, Research Institute for Children’s Health, Shahid Beheshti University of Medical Sciences, Tehran, Iran
3 Pediatric Surgery Research Center, Institute for Children’s Health, Shahid Beheshti University of Medical Sciences, Tehran, Iran
4 Pediatric Nephrology Research Center, Research Institute for Children’s Health, Shahid Beheshti University of Medical Sciences, Tehran, Iran
Abstract
Multicystic dysplastic kidney (MCDK) is a congenital kidney abnormality with an overall incidence rate of 1/4300 live births that is more prevalent in males than females. Here, we describe a rare case of bilateral MCDK complicated by hypertension, severe vesicoureteral reflux (VUR), and urinary tract infection (UTI), who stabilized during hospitalization with prospective kidney transplantation due to poor prognosis. Since bilateral MCDK is a rare disease with numerous complications and a poor prognosis, patient symptom management and treatment may be more challenging.
Implication for health policy/practice/research/medical education:
The multicystic dysplastic kidney (MCDK) frequently results in death in infancy, our case report could be a new step toward managing complicated bilateral MCDK manifestations, especially for improved survival.
Please cite this paper as: Pourpashang P, Hosseini Tabatabaei SMT, Fallahi M, Mohajerzadeh L, Zahmatkesh A. An infant girl with bilateral multicystic dysplastic kidney: a case report. J Nephropathol. 2025;14(1):e21432. DOI: 10.34172/jnp.2023.21432.